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Congenital simple hamartoma of RPE

Color retinography (Clarus 700, Zeiss, detail): Small brownish-black pigmented lesion in the macular area.

Optical coherence tomography (Cirrus-HD 5000, Zeiss) Protruding hyperreflective lesion in the inner retina with abrupt margins and a posterior hyporeflective acoustic shadow.

Description

Simple hamartoma of the retinal pigment epithelium is a highly pigmented, flat, solitary lesion of a congenital and benign nature, very rare.

OCT shows a characteristic pattern, which together with fundus imaging techniques allows differentiation from other more common fundus lesions. The visual prognosis is usually good, especially in cases with extrafoveal location.

Comments

Congenital simple RPE hamartoma is a little-known lesion that must be taken into account in the differential diagnosis of pigmented lesions of the fundus.

Indication

A 54-year-old male with type 2 DM, a history of simple DR and macular edema, who presented a pigmented macular lesion on fundus examination. Imaging tests and OCT showed a pattern suggestive of simple RPE hamartoma.